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Urticaria, Cholinergic

定義: 病態生理: 鑑別: 類天疱瘡 多型紅斑 マストサイトーシス 蕁麻疹様血管炎 診断・治療:

Urticaria, Acute

定義: 掻痒を伴う一過性の膨疹[wheal,hives]。 症状が6週間を過ぎて持続する場合、Urticaria,Chronicと称される。*1 膨疹が固定され24時間以上持続する場合、蕁麻疹様血管炎や類天疱瘡を考える。 病態生理: 免疫介在性(immune-mediated)の蕁麻疹 肥満細胞…

X-linked Agammaglobulinemia (XLA)

定義: X染色体上のBTK(Bruton tyrosine kinase)遺伝子の変異。 伴性劣性遺伝のため、男児のみ(1/25万)発症。女児には決して発症しない。 病態生理: BTKはpre-B細胞から成熟B細胞への分化に必須。患者は抗体を産生できない。 症状: 母親由来のIgGがなくな…

Atopic dermatitis (AD)

詳細省略。 罹患率は子供10〜20%程度、成人1%程度。 患者の1/3が喘息を併発。1/3がアレルギー性鼻炎を併発。 血液検査が必要となることは少なく、アレルギー検査(RAST)の有用性も低い。 乾燥型には特に軟膏基材の外用薬が推奨される。 カルシニューリン・イ…

Hereditary Angioedema (HAE)

定義: 常染色体優性遺伝のC1-INH欠損症。10万人に1〜2名。 HAE typeI・・・C1-INHの産生量減少。患者の85%。 HAE typeII・・・機能しないC1-INHの産生。患者の15%。 HAE typeIII・・・エストロゲン依存性。女性にのみ起こるタイプ。激稀。 病態生理: AAE参…

Acquired Angioedema (AAE)

定義: 後天的にC1 inhibitor(C1-INH)*1の機能不全を来したもの。 AAE typeI(AAE-I)・・・他の疾患(特にB細胞の増殖異常)に伴う二次的なもの。 AAE typeII(AAE-II)・・・C1-INHの自己抗体の存在。 病態生理: C1-INHは、C1、第XIIa因子*2、カリクレイン*3の…

ALLERGY and IMMUNOLOGY

Angioedema, Acquired Angioedema, Hereditary Atopic Dermatitis Bruton Agammaglobulinemia Common Variable Immunodeficiency Complement Receptor Deficiency Contact Dermatitis, Allergic Contact Dermatitis, Irritant Drug Eruptions Drug-Induced P…

MALIGNANT NEOPLASMS

Actinic Keratosis Arsenical Keratosis Basal Cell Carcinoma Bowen Disease Dermatofibrosarcoma Protuberans Eccrine Carcinoma Erythroplasia of Queyrat (Bowen Disease of the Glans Penis) Extramammary Paget Disease Keratoacanthoma Langerhans Ce…

BENIGN NEOPLASMS

Acquired Digital Fibrokeratoma Acrochordon Acrokeratosis Verruciformis of Hopf Angiokeratoma Circumscriptum Angiokeratoma of the Scrotum Apocrine Hidrocystoma Atypical Fibroxanthoma Atypical Mole (Dysplastic Nevus) Birt-Hogg-Dube Syndrome …

PARASITIC INFECTIONS

Cutaneous Larva Migrans Filariasis Leishmaniasis Lice Onchocerciasis (River Blindness) Protothecosis, Cutaneous Scabies Strongyloidiasis Tungiasis

FUNGAL INFECTIONS

Actinomycosis Aspergillosis Candidiasis, Chronic Mucocutaneous Candidiasis, Cutaneous Chromoblastomycosis Coccidioidomycosis Cutaneous Cryptococcus Eumycetoma (Fungal Mycetoma) Favus Lobomycosis Majocchi Granuloma Mycetoma Piedra Pityrospo…

VIRAL INFECTIONS

Bowenoid Papulosis Chickenpox Childhood HIV Disease Cowpox Infection, Human Cutaneous Manifestations of HIV Disease Cutaneous Manifestations of Hepatitis C Dengue Enteroviral Infections Epidermodysplasia Verruciformis Erythema Infectiosum …

BULLOUS DISEASES

Bullous Disease of Diabetes Bullous Disease of Dialysis Bullous Pemphigoid Cicatricial Pemphigoid Dermatitis Herpetiformis Drug-Induced Bullous Disorders Epidermolysis Bullosa Epidermolysis Bullosa Acquisita Familial Benign Pemphigus (Hail…

CONECTIVE TISSUE DISEASES

CREST Syndrome Dermatomyositis Eosinophilia-Myalgia Syndrome Eosinophilic Fasciitis Lupus Erythematosus, Acute Lupus Erythematosus, Bullous Lupus Erythematosus, Discoid Lupus Erythematosus, Drug-Induced Lupus Erythematosus, Subacute Cutane…

COSMETICS

Cosmeceuticals Cosmetics Moisturizers Nail Cosmetics Nonlaser Hair Removal Techniques Skin Lightening and Depigmenting Agents Skin and Hair Cleansers

DISEASE OF ADNEXA

Acne Conglobata Acne Fulminans Acne Keloidalis Nuchae Acne Vulgaris Acneiform Eruptions Alopecia Areata Alopecia Mucinosa Anagen Effluvium Androgenetic Alopecia Bromhidrosis Chromhidrosis Congenital Hypertrichosis Lanuginosa Disseminate an…

DISEASE OF DERMIS

Ainhum Anetoderma Atrophoderma of Pasini and Pierini Balanitis Xerotica Obliterans Cutaneous Manifestations of Smoking Cutis Laxa (Elastolysis) Elastosis Perforans Serpiginosum Knuckle Pads Kyrle Disease Lichen Myxedematosus Pachydermoperi…

DISEASE OF ORAL MUCOSA

Angina Bullosa Hemorrhagica Aphthous Stomatitis Bacterial Mouth Infections Cancers of the Oral Mucosa Candidiasis, Mucosal Cheilitis Glandularis Cheilitis Granulomatosa (Miescher-Melkersson-Rosenthal Syndrome) Chemotherapy-Induced Oral Muc…

DISEASE OF SUBCUTANEOUS TISSUE

Adiposis Dolorosa Cold Panniculitis Erythema Gyratum Repens Erythema Nodosum Lipodystrophy, HIV Lipodystrophy, Localized Lipodystrophy, Progressive Piezogenic Pedal Papules Subacute Nodular Migratory Panniculitis (Vilanova Disease) Subcuta…

DISEASE OF VESSELS

Acquired Progressive Lymphangioma Actinic Purpura Angioendotheliomatosis Angiolymphoid Hyperplasia with Eosinophilia Angioma Serpiginosum Blue Rubber Bleb Nevus Syndrome Capillary Malformation Cherry Hemangioma Churg-Strauss Syndrome (Alle…

ENVIRONMENTAL

Acrodynia Animal Bites Bedbug Bites Black Heel (Calcaneal Petechiae) Black Widow Spider Bite Botanical Dermatology Brown Recluse Spider Bite Burns, Chemical Burns, Electrical Clavus Corns Cutaneous Manifestations Following Exposures to Mar…

INTERNAL MEDICINE

Acrokeratosis Neoplastica Acromegaly Addison Disease Amyloidosis, Primary Systemic Calciphylaxis Carney Syndrome Cowden Disease (Multiple Hamartoma Syndrome) Cronkhite-Canada Syndrome Cutaneous Cholesterol Emboli Cutaneous Manifestations o…

LYMPHOMA AND RELATED PROCESSES

Angioimmunoblastic Lymphadenopathy With Dysproteinemia Cutaneous CD30+ (Ki-1) Anaplastic Large-Cell Lymphoma Drug-Induced Pseudolymphoma Syndrome Jessner Lymphocytic Infiltration of the Skin Kimura Disease Lymphocytoma Cutis Lymphomatoid P…

METABOLIC DISEASES

Acanthosis Nigricans Acrodermatitis Enteropathica Amyloidosis, Lichen Amyloidosis, Macular Amyloidosis, Nodular Localized Cutaneous Angiokeratoma Corporis Diffusum (Fabry Syndrome) Avitaminosis A Calcinosis Cutis Carotenemia Erythropoietic…

MYCOBACTERIAL INFECTIONS

Atypical Mycobacterial Diseases Buruli Ulcer Cutaneous Tuberculosis Leprosy Mycobacterium Avium-Intracellulare Infection Mycobacterium Marinum Infection of the Skin Papulonecrotic Tuberculids

NAILS

Clubbing of the Nails Congenital Onychodystrophy of the Index Fingers Muehrcke Lines of the Fingernails Nail-Patella Syndrome Onycholysis Onychomycosis Pachyonychia Congenita Paronychia

PAPULOSQUAMOUS DISEASES

Axillary Granular Parakeratosis Confluent and Reticulated Papillomatosis Erythroderma (Generalized Exfoliative Dermatitis) Hyperkeratosis Lenticularis Perstans (Flegel Disease) Hyperkeratosis of the Nipple and Areola Keratosis Follicularis…

PEDIATRIC DISEASES

Acrokeratoelastoidosis Acropustulosis of Infancy Acute Hemorrhagic Edema of Infancy Albright Syndrome Alezzandrini Syndrome Aplasia Cutis Congenita Asymmetric Periflexural Exanthem of Childhood Ataxia-Telangiectasia Atrophia Maculosa Vario…

PHOTO-RELATED DISEASE

Actinic Prurigo Berloque Dermatitis Chondrodermatitis Nodularis Helicis Colloid Milium Ephelides (Freckles) Favre-Racouchot Syndrome (Nodular Elastosis with Cysts and Comedones) Hydroa Vacciniforme Phytophotodermatitis Poikiloderma of Civa…